Search on: DIOXYGENASE, PROCOLLAGEN-PROLINE 
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Descriptor English:   Procollagen-Proline Dioxygenase 
Descriptor Spanish:   Procolágeno-Prolina Dioxigenasa 
Descriptor Portuguese:   Pró-Colágeno-Prolina Dioxigenase 
Synonyms English:   Procollagen Prolyl 4-Hydroxylase
4-Hydroxylase, Procollagen Prolyl
Dioxygenase, Procollagen-Proline
Hydroxylase, Protocollagen Prolyl
Procollagen Proline Dioxygenase
Procollagen Prolyl 4 Hydroxylase
Prolyl 4-Hydroxylase, Procollagen
Prolyl Hydroxylase, Protocollagen
Protocollagen Prolyl Hydroxylase  
Tree Number:   D08.811.682.690.416.617.750
D08.811.682.690.708.694.750
Definition English:   A mixed-function oxygenase that catalyzes the hydroxylation of a prolyl-glycyl containing peptide, usually in PROTOCOLLAGEN, to a hydroxyprolylglycyl-containing-peptide. The enzyme utilizes molecular OXYGEN with a concomitant oxidative decarboxylation of 2-oxoglutarate to SUCCINATE. The enzyme occurs as a tetramer of two alpha and two beta subunits. The beta subunit of procollagen-proline dioxygenase is identical to the enzyme PROTEIN DISULFIDE-ISOMERASES. 
See Related English:   Protein Disulfide-Isomerases
 
History Note English:   94; was PROLINE HYDROXYLASE 1972-93 (Prov 1972-73); PROLINE,2-OXOGLUTARATE 4-DIOXYGENASE was PROLINE,2-OXOGLUTARATE DIOXYGENASE see PROLINE HYDROXYLASE 1977-93 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   31898 
Unique Identifier:   D011393 

Occurrence in VHL:
 

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